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Hereditary Elliptocytosis Title Ñ Hereditary Elliptocytosis Definition Ñ Hereditary haemolytic anaemia Characterised by: Ñ The presence of elliptocytes Aetiology Ñ Autosomal dominant inheritance Clinical Features Ñ Similar to hereditary spherocytosis but milder features Management Control Surgery Ñ Only a few patients require splenectomy
Hereditary Elliptocytosis
Title
Ñ Hereditary Elliptocytosis
Definition
Ñ Hereditary haemolytic anaemia
Characterised by:
Ñ The presence of elliptocytes
Aetiology
Ñ Autosomal dominant inheritance
Clinical Features
Ñ Similar to hereditary spherocytosis but milder features
Management
Control
Surgery
Ñ Only a few patients require splenectomy
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